Visual snow syndrome
Keywords:Visual snow syndrome, case reports
Visual snow syndrome (VSS) is a rare clinical condition characterized by persistent positive visual phenomena in both eyes – multiple flickering small dots involving the entire visual field. VSS is predominantly observed at a young age, with onset most often in the third decade. The females are more commonly affected. The pathophysiology of the syndrome is unclear. The neurological and ophthalmological examination, as well as imaging studies of the brain are normal.
In the present publication, we present 5 patients (3 males and 2 females, mean age at examination 23,8 ± 7,08 years) with a clinical diagnosis of VSS. The average age of onset of their complaints (appearance of „permanent shining and flickering spots” in the entire vision field, simultaneously in both eyes, is 17,0 ± 8,09 years. In all patients, the neuro-ophthalmological status, including best corrected visual acuity, biomicroscopy of the anterior segment of the eye, tonometry, ophthalmoscopy, assessment of oculomotor movements, and at discretion, optical coherence tomography (OCT), etc. are normal. The magnetic resonance imaging of the brain, performed in all patients, as well as electroencephalography demonstrate normal finding. The clinical condition of the patients is monitored dynamically.
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